EEG in Epilepsy: Dravet Syndrome
- Roya Tompkins
- 3 days ago
- 1 min read
When can a febrile seizure be concerning?
In the rare circumstance that it is Dravet Syndrome.
Dravet syndrome is classified as a developmental and epileptic encephalopathy (also known as a DEE).
Seizures in Dravet syndrome usually begin during the first 2-15 months of life, often in the presence of a fever. The seizures are frequently prolonged, and are not well managed with current medications. Also, the seizures change over time as the patient ages.
What might we expect to see on the EEG?
In the first year of life the EEG may be normal; however as the child ages the abnormalities may appear.
Background slowing
Photic-sensitivity
Generalized spike and wave discharges
Focal or multi-focal abnormalities
Seizure types including myoclonic and atypical absence seizures appearing between the age of 1 and 4 years.
and episodes of Status Epilepticus are common before the age of 5.
Some common issues associated with Dravet syndrome include:
Prolonged seizures
Frequent seizures
Developmental delays
Movement and balance issues
Orthopedic conditions
Delayed language and speech issues
Growth and nutrition issues
Sleeping difficulties
Chronic infections
Disruptions of the autonomic nervous system which can lead to difficulty regulating body temperature, heart rate, blood pressure, and other issues
Current treatment options are limited; however, early diagnosis, treatment guidelines, new anti-seizure medications, and clinical studies for gene-targeted therapies are all improving the future outlook for patients with Dravet syndrome.
Roya Tompkins, MS, REEG/EPT, RPSGT
Resources:
Dravet Foundation
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